List
Asboe-Hansen sign: Bulla spread
sign in pemphigus
Acro-osteolysis:
Scleroderma
Apple jelly
nodules in nasal septum: Lupus vulgaris
Arnold head: Cleidocarnial
dysplasia
Ash-leaf spots:
Tuberous sclerosis
Auspitz sign:
Psoriasis
Bald tongue of
Sandwith: Pellagra
Bird facies: Treacher-collins
syndrome
Brazillian wild
fire: Pemphigus foliaceus
Buffalo hump: Cushing’s
syndrome
Bull neck:
Diphtheria
Bull’s eye
lesion: Steven-Johnson syndrome
Bull’s teeth:
Taurodontism
Butterfly shaped
lesion on malar bone: Sytemic lupus erythematous, Erysipelas
Button-hole sign:
Neurofibromatosis
Café au lait spots – coast of California:
Neurofibromatosis
Café au lait spots – coast of Maine: Fibrous dysplasia
Carpet tack
lesions: Discoid lupus erythematosus
Cerebriform
tongue: Pemphigus vegetans
Charcot’s triad:
Seen in multiple sclerosis, characterized by intention tremor, nystagmus,
dysarthria
Chipmunk facies:
Thalassemia
Chovstek’s sign:
Hypoparathyrodism
Circus rubber
man: Ehler-Danlos syndrome
Claw hands:
Scleroderma
Clover leaf
skull deformity: Crouzon syndrome, Apert’s syndrome
Compy’s sign:  Measles
Cobble stone
appearance: Lymphangioma, Inflammatory papillary hyperplasia, Heck’s disease
Coup de saber:
Facial hemiatrophy, Scleroderma
CREST: Scleroderma
Crowe’s sign: Neurofibromatosis
Cupids bow:
Double lip
Dew drop on rose
petal: Varicella
Erythema
nodosum: Coccidiodiomycosis, sarcoidosis
Exercise bone:
Traumatic myositis ossificans
Eyes upturned to
heaven: Cherubism
Facies leprosa:
Leprosy
Farmer’s skin:
Solar elastosis
Fetal facies: Robinow
syndrome
Fine pink
colored glistening scales: Pityriasis rosea
Fish facies: Treacher-Collins
syndrome
Forschemmier sign: Rubella
Fournier’s
molars: congenital syphilis
Frog facies:
Crouzon syndrome
Gorlin sign: Ehler
-Danlos Syndrome
Grains of salt
on a red background: Measles
Grattage sign:
Psoriasis
Hamman’s crunch:
Cervicofacial emphysema
Harelip: Cleft
lip
Hebra nose:
Rhinoscleroma
Herald spots: Pityriasis
rosea
Higomenakis’s sign: Congenital syphilis
Hockey stick
deformity of femur: Fibrous dysplasia
Hunter’s
glossitis: Pernicious anemia
Hutchinson’s sign: Herpes zoster
Hutchinson’s triad: Congenital syphilis with Hypoplasia
of incisor (Pegged laterals, screw driver shaped central incisor and mulberry molars),
Eighth nerve deafness and Interstitial keratitis.
Iris lesion: Steven-Johnson
syndrome
Iris pearl’s:
Leprosy
Koebner
phenomenon: Desquamative gingivitis, Lichen planus, pemphigus, Epidermolysis
bullosa dystropica
Koplik’s spots: Measles
Leonine facies:
Leprosy
Leontiasis
ossea: Paget’s disease
Leser-Trelat’s sign: Seborrheic
keratosis, internal malignancy
Lisch nodules:  Neurofibromatosis
Livedo
reticularis: Systemic lupus erythematosus
Lock jaw:
Tentanus
Longitudinal
lines in nails: Darrier’s disease
Luetic
glossitis: Syphilis
Lupus pernio:
Sarcoidosis
Magenta tongue:
Riboflavin deficiency
Maldon teeth:
Flurosis
Mask like face: Systemic
sclerosis, Periodic paralysis, Parkinsonism, Facial palsy.
Millian sign:
Erysipelas
Mitten hands: Apert’s
syndrome
Moeller’s
glossitis: Pernicious anemia
Mongloid
appearance: Down’s syndrome, Thalassemia
Moon facies:
Cushing syndrome
Moth eaten
alopecia: Secondary syphilis, Tinea capitis infection.
Mulberry molars:
Syphilis
Mulberry like
ulcerations: Paracoccidiodiomycosis
Myopathic
facies: Dystrophic myotonia
Nail fold
telangiectasia: Scleroderma, Systemic lupus erythematosus
Nikolsky’s sign:
Epidermolysis bullosa, pemphigus, Severe Steven –Johnson syndrome, Prophyria,
Toxi Epidermolysis Necrosis, Staphylococci Scalded skin syndrome
Oil drop sign:
Psoriasis
Ollendorf sign: Secondary syphilis.
Onycholysis:
Psoroasis
Papyraceous
scarring: Ehler-Dahlos syndrome
Parrot’s beak
nose: Crouzon syndrome
Pastia’s lines:
Scarlet fever
Percussion
contraction: Congenital myotonia
Petrified man:
Myositis  ossificans progressiva
Pink teeth:
Internal resorption, Leprosy
Pterygium of
nails: Lichen planus
Raspberry
tongue: Scarlet fever
Red strawberry
tongue: Scarlet fever
Rodent facies: Thalassemia
Shagreen patch:
Tuberous sclerosis
Shepard’s crook
sign: Fibrous dysplasia
Simian stance:
Paget’s disease
Skin with sand
paper texture: Scarlet fever
Snail track
ulcers: Syphilis
Socks feet:
Apert’s syndrome
Steinberg’s
sign: Marfan syndrome
Strawberry
gingivitis: Wegner’s granulomatosis
Submerged teeth:
Ankylosed teeth
Sulphur like
granules in pus: Actinomycosis, Botryomycosis
Sun burn with
goose pimples appearance: Scarlet fever
Swan neck:
Dystrophic myotonia
Tapir lips: Mild
restricted muscular dystrophy
Target lesion:
Steven-Johnson syndrome
White strawberry
tongue: Scarlet fever
Woronhoff’s ring: Halo around any
skin lesion
Wrist sign:
Marfan syndrome

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